Authors: Kuroda Y
Title: Foix-Chavany-Marie syndrome: Case reports with literature review
Source: Journal of Medical Speech Language Pathology 2007 15(2): 137-147
Year: 2007
Research Design: Single Case Design

Foix-Chavany-Marie syndrome (FCMS), also known as the anterior operculum syndrome, is considered the cortical type of pseudobulbar palsy, which is characterized by severe dysarthria and bilateral paralysis of the facial, lingual, pharyngeal, and masticatory muscles with automatic-voluntary dissociation. Although FCMS appears to be a well-defined clinical entity, there are a few equivocal points. First, the distinction between FCMS and the noncortical type of acute pseudobulbar palsy is not clearly defined. Second, there is some confusion in the diagnostic classification of the developmental, reversible, and neurodegenerative forms of FCMS or similar syndromes. Third, some ambiguity exists regarding the terminologies used for certain symptoms of FCMS. In this article, two FCMS cases are presented, along with reviews of the literature on FCMS. The purpose of this study is to draw attention to this syndrome and to discuss its clinical characteristics, associated lesions, and prognosis.

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